This book aims to be a complete guide to diagnose, manage, and treat rare lung diseases encountered by practicing pulmonologists and trainees. It extensively covers the "more common" of the rare lung diseases, categorizing them based on developmental lung anomalies in adults, airway disorders, diffuse parenchymal lung diseases, neoplasms, rare vascular disorders, and other miscellaneous conditions. This comprehensive review facilitates the study and understanding of this complex and diverse set of disorders, focusing on differential diagnosis, evidence-based discussions of management algorithms, and thoughtful analysis of treatment options.
Key Features
* Reviews multiple rare lung diseases, including ones acquired congenitally to be expressed in old age
* Enriched with case studies and illustrations to guide respiratory physicians and trainees to devise an effective treatment plan
*Focuses on concerned investigations, with a section on the role of new procedures in management
Author(s): Sujith V. Cherian, Anupam Kumar
Edition: 1
Year: 2023
Language: English
Commentary: TRUE PDF
Tags: Rare Lung Diseases; Pulmonary & Critical Care Medicine; Respiratory Medicine
Cover
Half Title
Title Page
Copyright Page
Dedication
Contents
Foreword
Preface
Editors
Contributors
1. Introduction
2. Developmental Lung Anomalies in Adults
PART A: RARE GENETIC LUNG DISEASES
3. Genetic Infiltrative Lung Diseases
4. Alpha-1 Antitrypsin Deficiency
PART B: RARE AIRWAY DISORDERS
5. Benign Central Airway Disorders
6. Bronchiolitis
7. Allergic Bronchopulmonary Aspergillosis (ABPA)
PART C: RARE PULMONARY VASCULAR DISEASES
8. Pulmonary Arteriovenous Malformations (PAVMs) and Hereditary Hemorrhagic Telangiectasia (HHT)
9. Diffuse Alveolar Hemorrhage (DAH) Syndromes
10. Pulmonary Veno-Occlusive Disease and Pulmonary Capillary Hemangiomatosis
PART D: RARE DIFFUSE PARENCHYMAL LUNG DISEASES
11. Pleuroparenchymal Fibroelastosis (PPFE)
12. Immunoglobulin G4-Related Lung Disease
13. Eosinophilic Lung Diseases
14. Hard Metal Lung Disease and Other Rare Occupational Lung Diseases
15. Adult Pulmonary Alveolar Proteinosis
PART E: RARE DIFFUSE CYSTIC LUNG DISEASES
16. Lymphangioleiomyomatosis
17. Lymphocytic Interstitial Pneumonia and Associated Cystic Lung Diseases
18. Birt–Hogg–Dubé Syndrome
19. Pulmonary Langerhans Cell Histiocytosis and Other Histiocytic Lung Diseases
PART F: RARE PULMONARY NEOPLASMS
20. Primary Pulmonary Lymphoproliferative Neoplasms
21. Diffuse Idiopathic Pulmonary Neuroendocrine Cell Hyperplasia
22. Pulmonary Amyloidosis
23. Primary Tracheal Tumors
PART G: RARE PLEURAL DISORDERS
24. Unusual Causes of Pleural Effusion
25. Thoracic Endometriosis
26. Tumors of the Pleura
Index
